Pulmonary Hypertension with COPD or Pulmonary Fibrosis

Pulmonary hypertension (PH) can occur in people who have chronic lung diseases, such as COPD (chronic obstructive pulmonary disease) or idiopathic pulmonary fibrosis (IPF).

The cause of PH was long thought to be due to chronically low oxygen levels, but the exact cause is not known.

Because the nature of these diseases is complex, they can be difficult to treat.

Treatment of Severe Pulmonary Hypertension with Chronic Lung Disease

Treating PH associated with chronic lung disease is challenging. Patients with lung disease do not necessarily respond the same way as patients without lung disease do.

It is important to weigh the risks and benefits of PH therapies in the setting of underlying lung disease.

Based on clinical experience and lack of evidence for great benefits in people with mild PH, the team at the UPMC Comprehensive Pulmonary Hypertension Program focuses on treating patients with severe PH.

People with severe PH are at highest risk of death and are most likely to be helped.

Given the complex nature of this diagnosis, we often recommend that patients:

In our program, we work closely with the Emphysema Clinical Research Center and Simmons Center for Interstitial Lung Disease, through which research studies often are available.

We are happy to evaluate patients for PH associated with chronic lung disease to explore available clinical trials and help form patient-specific treatment plans.

Our expertise in PH, COPD, pulmonary fibrosis, and lung transplantation allows our patients to explore all available treatment options for this complicated disease.

Make an Appointment Today

To schedule an appointment at the UPMC Comprehensive Pulmonary Hypertension Program, contact us at:

Learn More About COPD and Other Breathing Disorders

UPMC Patient Education Materials on Breathing Disorders:

Schedule an Appointment

To schedule an appointment with the UPMC Comprehensive Pulmonary Hypertension Program team, call toll-free at
1-877-PH4-UPMC, or email PHprogram@upmc.edu.​​

UPMC | Affiliated with the University of Pittsburgh Schools of the Health Sciences | Supplemental content provided by Healthwise, Incorporated. To learn more, visit www.healthwise.org

For help in finding a doctor or health service that suits your needs, call the UPMC Referral Service at 412-647-UPMC (8762) or 1-800-533-UPMC (8762). Select option 1.

UPMC is an equal opportunity employer. UPMC policy prohibits discrimination or harassment on the basis of race, color, religion, ancestry, national origin, age, sex, genetics, sexual orientation, gender identity, marital status, familial status, disability, veteran status, or any other legally protected group status. Further, UPMC will continue to support and promote equal employment opportunity, human dignity, and racial, ethnic, and cultural diversity. This policy applies to admissions, employment, and access to and treatment in UPMC programs and activities. This commitment is made by UPMC in accordance with federal, state, and/or local laws and regulations.

Medical information made available on UPMC.com is not intended to be used as a substitute for professional medical advice, diagnosis, or treatment. You should not rely entirely on this information for your health care needs. Ask your own doctor or health care provider any specific medical questions that you have. Further, UPMC.com is not a tool to be used in the case of an emergency. If an emergency arises, you should seek appropriate emergency medical services.

Pittsburgh, PA, USA | UPMC.com